68.

69.

70.

71.

72.

3 month old baby, born of second degree consanguineous marriage was brought with c/o
feeding difficulty and poor weight gain. O/E — Thin and floppy infant with large protruding
tongue, taccycardia and taccypnea +, cardiomegaly ejection systolic murmur at upper
Lt. sternal border. Hepatomegaly +

Which among the following is a most likely cause?
(A) Infantile Pompe Disease
(B) Von Gierke disease
(C) Phenyl] Ketonuria
(D) Mucopolysaccharidosis

A 1 month old baby with C/O non bilious vomiting 81706 234 week of life. O/E — Thin,
emaciated and dehydrated. Abdomen — distended with visible peristalsis in upper abdomen.
USG abdomen clinched the diagnosis.

What is the most appropriate step to be taken next?
(ಹ) Refer to surgeon immediately (B)_ Correct dehydration
(C) Correct dyselectrolytemia (D) Both (B) and (C)

Which among the following is a criterion for severe acute malnutrition (SAM)?
(A) Weight < 3"4 Centile (B) MUAC < 12.5 cms
(C) Weight for length/height <—3 SD ൯) Allof the above

A3 year old girl was diagnosed to have oligoarticular Rheumatoid arthritis. She was found to
be ANA Positive. Which organ is to be urgently evaluated and frequently followed up to avoid
complications?

(^) Eye (B) Heart

(C) Hemopoetic system (D) Kidney

1% year old child with fever and skin rash for past 6 days. O/E — Child irritable,
b/I conjunctival congestion, cheilitis with oral mucosal congestion. Lt posterior cervical lymph
node enlarged, slightly tender. Generalized maculopapular rashes present.
No hepatosplenomegaly. Initial investigations revealed marked increase in acute phase
reactants. What is the most important investigation you will order next?

(^) Blood culture (B) ECHO
(C) Chest X-ray (D) USG abdomen

159/2023 16 A